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{"id":7132,"date":"2015-12-23T10:08:16","date_gmt":"2015-12-23T08:08:16","guid":{"rendered":"https:\/\/www.coolkadin.com\/?p=7132"},"modified":"2015-12-23T10:08:16","modified_gmt":"2015-12-23T08:08:16","slug":"gastrosizis-gastroschisis","status":"publish","type":"post","link":"https:\/\/www.coolkadin.com\/gastrosizis-gastroschisis.html","title":{"rendered":"Gastro\u015fizis (Gastroschisis)"},"content":{"rendered":"

1 ) Gastro\u015fizis (Gastroschisis) Nedir?<\/strong><\/p>\n

Bebe\u011fin kordonunun hemen yan b\u00f6lgesinde bulunan bir a\u00e7\u0131kl\u0131ktan, ba\u011f\u0131rsaklar\u0131n kar\u0131n\u0131n d\u0131\u015far\u0131s\u0131na \u00e7\u0131kmas\u0131 durumuna gastro\u015fizis ismi verilir. Kromozomal anormallikler le herhangi bir alakas\u0131 bulunmaz. Yaln\u0131z, ba\u011f\u0131rsaklar ile alakal\u0131 d\u00fc\u011f\u00fcmlenme veya ba\u011f\u0131rsa\u011f\u0131n bir k\u0131sm\u0131n\u0131n olu\u015fumunu tamamlayamamas\u0131 gibi sorunlara neden olabilir. Bu sorun ile d\u00fcnyaya gelen bebeklerin, ya\u015fama oranlar\u0131 olduk\u00e7a y\u00fcksektir. Bu oran, yakla\u015f\u0131k %80 ile %100 civar\u0131ndad\u0131r.<\/p>\n

2 ) Gastro\u015fizis e Ne kadar s\u0131kl\u0131kta rastlan\u0131r?<\/strong><\/p>\n

Gastro\u015fizis, yakla\u015f\u0131k olarak 10 bin hamilelikte bir g\u00f6r\u00fclen \u00e7ok \u00e7ok fazla rastlanmayan bir durumdur. Bu problemin bir sonra ki hamilelikte de meydana gelme olas\u0131l\u0131\u011f\u0131 ise, yakla\u015f\u0131k %3 ile % 5 civar\u0131nda de\u011fi\u015fmektedir.<\/p>\n

3 ) Nas\u0131l Te\u015fhis edilir?<\/strong><\/p>\n

Ultrason yard\u0131m\u0131 sayesinde, omfalosel ve gastro\u015fizis te\u015fhisi yap\u0131labilir. Minimum, hamilelik d\u00f6neminin 3. ay\u0131ndan sonra te\u015fhis edilmesi m\u00fcmk\u00fcnd\u00fcr. Bu d\u00f6neme dek, ba\u011f\u0131rsaklar\u0131n d\u0131\u015far\u0131da g\u00f6r\u00fcnmesi zaten normal olarak kabul edilir. Bu duruma ise, \u201cfizyolojik herni\u201d ismi verilir. Gastro\u015fizis ve omfaloselde, anne kan\u0131nda AFP (alfafetoprotein) \u00f6l\u00e7\u00fcm\u00fcn\u00fcn de\u011ferleri y\u00fcksek bulunarak, polihidramnios (amniyon suyu fazlal\u0131\u011f\u0131) ile kar\u015f\u0131la\u015f\u0131labilir.<\/p>\n

4 ) Gastro\u015fizis in bebek \u00fczerinde ki Riskleri nelerdir?<\/strong><\/p>\n

Gastro\u015fizis vakas\u0131 ile kar\u015f\u0131la\u015f\u0131lmas\u0131 halinde, bebekte erken do\u011fuma, b\u00fcy\u00fcme gerili\u011fine veya \u00f6l\u00fcme dahi neden olabilir. Bu sebepten dolay\u0131, d\u00fczenli bir \u015fekilde anne aday\u0131n\u0131n ultrason takiplerini yapt\u0131rmalar\u0131 gerekmektedir.<\/p>\n

5 ) B\u00f6yle bir durumda Do\u011fum nas\u0131l olmal\u0131d\u0131r?<\/strong><\/p>\n

Gastro\u015fizis ile kar\u015f\u0131la\u015f\u0131lm\u0131\u015f olan bebeklerin do\u011fumunda, sezaryen ile do\u011fumun ger\u00e7ekle\u015ftirilmesi tavsiye edilmektedir. Do\u011fumun, bebe\u011fin ameliyat\u0131n\u0131n sa\u011flanabilece\u011fi bir merkezde yapt\u0131r\u0131lmas\u0131 gerekmektedir.<\/p>\n

6 ) Gastro\u015fizis defektinin Tedavisi m\u00fcmk\u00fcn m\u00fc?<\/strong><\/p>\n

Tedavinin yap\u0131labilmesi i\u00e7in, bebe\u011fin d\u00fcnyaya gelmesinin ard\u0131ndan ameliyat edilmesi gerekmektedir.<\/p>\n

Ger\u00e7ekle\u015ftirilen ameliyatlar\u0131n, b\u00fcy\u00fck bir \u00e7o\u011funlu\u011funda ba\u015far\u0131 elde dilir. Ancak, bebekte bu rahats\u0131zl\u0131\u011fa e\u015filk eden ba\u015fka bir anomalilerin bulunmas\u0131 halinde, bebe\u011fin durumu bu anomalilerin ne oldu\u011funa ve ciddiyetine bak\u0131larak de\u011fi\u015fiklik g\u00f6sterir. Bebekte omfalosel haricinde ba\u015fka bir anormallik bulunmuyor ise, bebe\u011fin yakla\u015f\u0131k %90 civar\u0131nda ya\u015fama \u015fans\u0131 bulunur. Beraberinde oligohidramnios veya polihidramnois (bebe\u011fin suyunun az veya fazla olmas\u0131) bulunuyor ise, kromozomal anomali riski de artar ve bu durumda bebe\u011fin ya\u015fama \u015fans\u0131 da azal\u0131r.<\/p>\n

7 ) OMFALOSEL (Omphalocele) Nedir?<\/strong><\/p>\n

Omfaloselde gastro\u015fizisten de\u011fi\u015fik olarak, bebe\u011fin ba\u011f\u0131rsaklar\u0131 kar\u0131n zar\u0131 (periton) ile \u00f6rt\u00fcl\u00fcd\u00fcr. Burada g\u00f6r\u00fclen as\u0131l sorun, kar\u0131n duvar\u0131nda yer alan kaslar\u0131n iyi kapanmamas\u0131 neticesinde meydana gelir. Omfalosel g\u00f6r\u00fclen bebeklerin gastro\u015fizisten farkl\u0131 olarak ortalama olarak %25 ile %50 civar\u0131nda ilave sorunlar ile de kar\u015f\u0131la\u015f\u0131labilmektedir. Bunlar genetik sorunlar (kromozomal anormallikler), konjenital diafragma hernisi ve kalp anomalileri olabilir. Bu nedenden dolay\u0131, gastro\u015fizisten ayr\u0131m\u0131 olduk\u00e7a \u00f6nemlidir. Omfaloselde amnisentez yap\u0131lmas\u0131na ihtiya\u00e7 duyulur. Fetal ekokardiyografi de yap\u0131lmal\u0131d\u0131r.<\/p>\n

Omfalosel farkl\u0131 boyutlarda olabilir. K\u00fc\u00e7\u00fck olanlarda, kar\u0131ndan f\u0131t\u0131kla\u015fan kesenin i\u00e7erisinde yaln\u0131zca ba\u011f\u0131rsaklar yer al\u0131rken, daha b\u00fcy\u00fck olanlarda ise, karaci\u011fer veya dalak da yer alabilmektedir.
\nuygulanan t\u00fcm tahlillerin ve amniosentezin neticesinde ve beraberinde gelen anomalilerin tamam\u0131 aile ile beraber konu\u015fularak, ailenin hamileli\u011fi sonland\u0131r\u0131lmas\u0131 veya devam etmesi hakk\u0131nda bilgisi al\u0131n\u0131r.<\/p>\n

8 ) Ay\u0131r\u0131c\u0131 tan\u0131 nas\u0131l yap\u0131lmaktad\u0131r?<\/strong><\/p>\n

Omfalosel ile gastro\u015fizis aras\u0131nda ay\u0131r\u0131c\u0131 bir tan\u0131n\u0131n yap\u0131lmas\u0131 gerekmektedir. Omfaloselde, bir kese vard\u0131r ve kar\u0131n organlar\u0131 bu kese i\u00e7erisinde bulunur. Gastro\u015fiziste ise, kar\u0131n duvar\u0131 tamam\u0131 ile a\u00e7\u0131k ve ba\u011f\u0131rsaklar karn\u0131n d\u0131\u015far\u0131s\u0131nda yer al\u0131r. Ancak omfalosel kesesinin y\u0131rt\u0131lmas\u0131 halinde, ay\u0131r\u0131c\u0131 tan\u0131n\u0131n yap\u0131lmas\u0131 zordur ve bu durumda \u015fu farkl\u0131l\u0131klar incelenerek ay\u0131r\u0131m\u0131n yap\u0131lmas\u0131 sa\u011flan\u0131r;<\/p>\n

* Omfalosel<\/strong><\/p>\n

Defekt, g\u00f6bek b\u00f6lgesinde yer al\u0131r, umbilikal kord kesesinin \u00fczerine \u00e7\u0131kar
\nHerni kesesi g\u00f6r\u00fcl\u00fcr
\nKaraci\u011fer ile ba\u011f\u0131rsaklar, hernie olur
\nBa\u011f\u0131rsa\u011f\u0131n y\u00fczeyi normal bir \u015fekilde g\u00f6zlenir
\nAbdominal kative daha k\u00fc\u00e7\u00fck g\u00f6zlenir
\nCiddi ek anormallikler fazlad\u0131r. Bu anormalliklerin i\u00e7erisinde en fazla kar\u015f\u0131la\u015f\u0131lan\u0131, kardiak anomalileridir.<\/p>\n

*Gastro\u015fizis<\/strong><\/p>\n

Herni kesesi g\u00f6zlenmez
\nDefekt g\u00f6be\u011fin sa\u011f b\u00f6lgesinde yer al\u0131r, g\u00f6bek ve umbilikal kordon normal yerindedir. Defekt ile g\u00f6be\u011fin aras\u0131nda normal kar\u0131n duvar\u0131 yer al\u0131r
\nEn fazla ince ba\u011f\u0131rsaklar\u0131n hernie oldu\u011fu g\u00f6zlenir
\nHernie ba\u011f\u0131rsak kal\u0131nla\u015farak k\u0131sal\u0131r
\nAbdominal kative daha yeterli bir b\u00fcy\u00fckl\u00fcktedir
\nCiddi olarak en anomalilere az rastlan\u0131r. En fazla rastlanan anomali ise, intestinal atreziler ile beraber, inmemi\u015f testislerdir<\/p>\n","protected":false},"excerpt":{"rendered":"

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